Rare Orphan Lung Diseases PDF Download

Written and edited by global leaders in this challenging field, Rare and Interstitial Lung Diseases: Clinical Cases and Real-World Discussions brings you up to date with the latest advances in complex or rare lung diseases managed on outpatient or inpatient respiratory or critical care units. Using a unique, case-based approach, a wide variety of cases are presented along with perspectives from a multidisciplinary team of experts who discuss therapeutic choices and rationales. This real-world approach allows the reader to become a virtual attending physician, simulating a realistic clinical reasoning process on the diagnosis, treatment, and follow-up of patients with rare and complex lung diseases. Reflects a nuanced, multidisciplinary, evidence-based approach to diagnoses, treatment options, and follow-up criteria for complex and rare pulmonary disorders such as idiopathic pulmonary fibrosis, interstitial lung disease related to connective tissue diseases, hypersensitivity pneumonitis, sarcoidosis, and pulmonary vascular disease. Each case includes onset of symptoms, diagnostic/therapeutic path, and discussions on the clinical choices made in accordance with evidence-based medical procedures. Describes each clinical and laboratory finding and features 150 images, including plain film, procedural photos, ultrasound images, CT scans, and histopathology specimens. Includes the most recent updates to international guidelines (ATS/ERS/JRS/ALAT) on idiopathic pulmonary fibrosis (IPF). Covers the progression of pulmonary fibrosis in patients with ILD other than IPF; the role of transbronchial lung cryobiopsy (TBLC) in obtaining a tissue diagnosis in patients with undiagnosed ILD; and the indications of antifibrosant drugs. A practical and interactive resource for pulmonologists, as well as critical care and internal medicine practitioners and fellows, thoracic surgeons, and thoracic radiologists. Any additional digital ancillary content may publish up to 6 weeks following the publication date.